Rapid and fulminant leptomeningeal spread following radiotherapy in diffuse intrinsic pontine glioma.
نویسندگان
چکیده
A 4-year-old male presented with rapid-onset cranial nerve palsy and ataxia. Brain magnetic resonance imaging (MRI) revealed a pontine mass lesion with discordant conventional and advanced imaging. A stereotactic core biopsy revealed glioblastoma with immunostaining suggestive of histone H3K27M and TP53 mutation, consistent with diffuse intrinsic pontine glioma. MRI 3 months after radiotherapy revealed extensive new leptomeningeal metastatic disease involving both the supra- and infratentorial brain, as well as the imaged portion of the spine. Tissue procured at the time of needle biopsy has undergone striking in vivo expansion as an orthotopic xenograft.
منابع مشابه
Subventricular spread of diffuse intrinsic pontine glioma - Online First - Springer
This is an excerpt from the content Diffuse intrinsic pontine glioma (DIPG) is the second most common malignant pediatric brain tumor and the leading cause of brain tumor death in childhood [1]. 80 % of DIPG tumors exhibit a specific mutation (H3K27M) in the genes encoding histone 3.1 or 3.3 [2, 3]. Standard therapy consisting of local radiotherapy to a dosage of 54–60 Gy extends median surviva...
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ورودعنوان ژورنال:
- Pediatric blood & cancer
دوره 64 8 شماره
صفحات -
تاریخ انتشار 2017