Rapid and fulminant leptomeningeal spread following radiotherapy in diffuse intrinsic pontine glioma.

نویسندگان

  • Christopher L Tinkle
  • Brent A Orr
  • John T Lucas
  • Paul Klimo
  • Zoltan Patay
  • Suzanne J Baker
  • Alberto Broniscer
  • Ibrahim Qaddoumi
چکیده

A 4-year-old male presented with rapid-onset cranial nerve palsy and ataxia. Brain magnetic resonance imaging (MRI) revealed a pontine mass lesion with discordant conventional and advanced imaging. A stereotactic core biopsy revealed glioblastoma with immunostaining suggestive of histone H3K27M and TP53 mutation, consistent with diffuse intrinsic pontine glioma. MRI 3 months after radiotherapy revealed extensive new leptomeningeal metastatic disease involving both the supra- and infratentorial brain, as well as the imaged portion of the spine. Tissue procured at the time of needle biopsy has undergone striking in vivo expansion as an orthotopic xenograft.

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عنوان ژورنال:
  • Pediatric blood & cancer

دوره 64 8  شماره 

صفحات  -

تاریخ انتشار 2017